Restrictive cardiomyopathy

Restrictive cardiomyopathy is characterized by impaired diastolic relaxation chamber, due to rigid walls of the heart chambers, thus, prevented them properly filling with blood.

The cause of

A large number of processes that cause infiltration and myocardial fibrosis can cause this disease. There are two forms of the disease: idiopathic, which is rare, and the secondary, whose causes are numerous: amyloidosis, sarcoidosis, endomyocardial fibrosis, Loefflerov hipereozinofilni endocarditis, carcinoid, and endocardial fibroelastoza hemochromatosis.

The clinical picture

Dominated by symptoms of heart failure, and often, right. It is located nabreklost neck veins, peripheral edema (swelling), hepatomegaly (enlarged liver), and sometimes ascites (presence of fluid in the abdomen). Often occurs dyspnea (shortness of breath), fatigue and edema. Heart sounds are quiet, there is tachycardia (rapid heartbeat) and frequent arrhythmia.

The disease is progredijentnog flow for several years, ending in death, mainly due to refractory heart failure.

Diagnosis

It is based on history, clinical findings, objective examination (tricuspid regurgitation murmur), ECG, x-ray, ultrasound and cardiac catheterization.

Treatment

Treatment is aimed at improving heart failure. Be conducted, with sparing patients the larger effort, the symptomatic treatment of heart failure with diuretics, digoxin, ACE inhibitors, antiarrhythmics. When the existence of the risk of systemic embolism should be given oral anticoagulant. Medical therapy is often ineffective, and sometimes need surgery consisting of excision of fibrotic endocardium and valve replacement.